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PO-04-017 LIMITED PREDICTIVE ABILITY OF CURRENT GUIDELINES FOR SUDDEN CARDIAC DEATH RISK IN PEDIATRIC HYPERTROPHIC CARDIOMYOPATHY

HeartRhythm

Sudden cardiac death represents a significant mortality factor in hypertrophic cardiomyopathy (HCM). Nevertheless, the validation of the existing risk prediction model in the pediatric population remains insufficiently explored.

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Potential impact of long-term ambulatory electrocardiographic monitoring on estimated sudden cardiac death risk in childhood hypertrophic cardiomyopathy

HeartRhythm

Identifying children with hypertrophic cardiomyopathy (HCM) at high risk for sudden cardiac death (SCD) is an important part of clinical care.1,2

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Mortality Patterns in Pediatric Pulmonary Vein Stenosis: Insights Into Right Ventricular Systolic Pressure Associations

Journal of the American Heart Association

All patients underwent cardiac catheterization, with 45 (80%) undergoing at least 1 interventional procedure. Causes of death included multiorgan failure (35%), progressive respiratory failure (20%), and sudden cardiac death (15%). 95% CI, 2.214.1];P<0.001). P<0.001).

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Myocardial Scarring and SCD in Young HCM Patients

American College of Cardiology

What is the association between late gadolinium enhancement (LGE) on cardiac magnetic resonance imaging (cMRI) and sudden cardiac death (SCD) in pediatric patients with hypertrophic cardiomyopathy (HCM), and does it add to pediatric SCD risk models?

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AP-482896-005 PREDICTORS OF INAPPROPRIATE SHOCKS IN PEDIATRIC PATIENTS WITH SUBCUTANEOUS ICDS

HeartRhythm

Subcutaneous ICDs (S-ICD) are a treatment option for the prevention of sudden cardiac death in pediatric patients. However, in a 2020 multicenter study of pediatric patients with a S-ICD found a risk of inappropriate shock (IS) double that of a large adult study. The S-ICD has limited programming options.

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PO-04-008 EPIDEMIOLOGY AND OUTCOME OF PEDIATRIC PATIENTS WITH INHERITED ARRHYTHMIAS IN KOREAN MULTICENTER STUDY

HeartRhythm

Inherited arrhythmias (IAs) account for a significant proportion of sudden cardiac death (SCD) in young patients without overt heart disease. To date, the studies of Asian pediatric population with IAs are rarely reported.

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Diagnostic approach to the Pediatric Brugada Syndrome: A survey of international common practice

HeartRhythm

The Brugada Syndrome (BrS) is a rare inherited disorder predisposing patients to arrythmia and sudden cardiac death. In 2014 a first comprehensive review of diagnostic and therapeutic strategies in the pediatric BrS was published 3. A considerable number of patients are already symptomatic in infancy 2.