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Pulmonary arterial hypertension in congenital heart disease

Heart BMJ

LEARNING OBJECTIVES Review the diagnostic pathway for pulmonary arterial hypertension (PAH) in congenital heart disease (CHD). Understand and interpret right heart catheterisation data in pulmonary hypertension related to CHD. Recognise the typical presentation of PAH in patients with CHD. 2 PAH encompasses conditions with.

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Raising the bar: triple therapy for pulmonary arterial hypertension associated with congenital heart disease

Heart BMJ

Pulmonary arterial hypertension related to congenital heart disease as a paradigm of complexity Pulmonary arterial hypertension related to congenital heart disease (PAH-CHD) really represents a paradigm of complexity.

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PO-01-044 ARRHYTHMIA OCCURENCE AFTER TRANSCATHETER PULMONARY VALVE REPLACEMENT IN CONGENITAL HEART DISEASE PATIENTS

HeartRhythm

Transcatheter pulmonary valve replacement (TPVR) has become a safe and effective alternative to surgical PVR in tetralogy of Fallot (TOF), isolated pulmonary stenosis (PS), and other congenital heart disease (CHD) variants.

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What are the Cyanotic Congenital Heart Diseases With Decreased Pulmonary Blood Flow?

All About Cardiovascular System and Disorders

Tetralogy of Fallot TOF with pulmonary atresia Pulmonary atresia with intact interventricular septum Tricuspid atresia Double outlet right ventricle Transposition of great arteries with ventricular septal defect and pulmonary stenosis Ebstein’s anomaly of tricuspid valve In DORV and tricuspid atresia, there are also variants with increased pulmonary (..)

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Hot Topics in Congenital and Pediatric Cardiology in the Year 2023

American College of Cardiology

This year saw exciting developments in the treatment of pediatric and congenital heart disease. Transcatheter pulmonary valve replacement (TPVR) continued to dominate the field of interventional cardiology.

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Insight into the research history and trends of total anomalous pulmonary venous connection: a bibliometric analysis

Journal of Cardiothoracic Surgery

Total anomalous pulmonary venous connection (TAPVC) is a rare congenital heart disease characterized by the inability of all pulmonary veins to connect to the left atrium. Our previous bibliometric article sum.

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Pulmonary arterial hypertension related to congenital heart disease with a left-to-right shunt: phenotypic spectrum and approach to management

Frontiers in Cardiovascular Medicine

Patients with pulmonary hypertension associated with a left-right shunt include a wide spectrum of pathophysiological substrates, ranging from those characterized by pulmonary over-circulation to those with advanced pulmonary vascular disease.