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Atrial arrhythmia and heart failure in congenital heart disease: a pas de deux with consequences

Heart BMJ

In adults with congenital heart disease (ACHD patients), atrial arrhythmias (AA) and heart failure (HF) are common. 1 Factors related to congenital heart disease, such as underlying anatomy, surgical repair technique and scars, can all be considered as AA substrates. In the current issue, Lauwers and coworkers 3 set out.

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Case Report: Complete AV block in two patients with a congenital absence of the right coronary artery: an unusual correlation

Frontiers in Cardiovascular Medicine

No previous reports have documented the coexistence of congenital absence of the RCA and complete AV block in the same patient.Case summariesCase 1 was a 52-year-old man with no significant past medical history who experienced syncope. The prevalence of complete atrioventricular (AV) block also appears to be low.

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Atrial arrhythmia and heart failure in adult patients with congenital heart disease: a retrospective cohort study

Heart BMJ

Background Atrial arrhythmias (AA) and heart failure (HF) are major causes of hospitalisation in adult congenital heart disease (ACHD). Dates of first AA and HF presentations were documented, and outcomes of RFA, including acute and long-term success, were assessed.

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Genetic syndromes associated with congenital heart disease

Heart BMJ

Congenital heart defects are the most common type of birth defect, affecting 1% of live births. The underlying cause of congenital heart disease is frequently unknown. However, advances in human genetics and genome technologies have helped expand congenital heart disease pathogenesis knowledge during the last few decades.

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Pregnancy and cardiovascular outcomes among patients post Fontan surgery: a 25-year single-centre retrospective cohort study

Open Heart

Methods We included adult patients who had undergone Fontan surgery for congenital heart disease and were pregnant between 1994 and 2021. Conclusions Over one-third of women with Fontan physiology in our cohort had a documented pregnancy. We examined maternal and obstetric outcomes.

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A review of literature of a functional, congenital intrathoracic kidney

Journal of Cardiothoracic Surgery

The rarest form of renal ectopia, the thoracic kidney, has been documented in only about 200 cases worldwide. There are four recognized causes of congenital thoracic renal ectopia: renal ectopia with an intact.

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Cardiovascular Management of Aortopathy in Children: A Scientific Statement From the American Heart Association

Circulation

Pathogeneses include connective tissue disorders, smooth muscle contraction disorders, and congenital heart disease, including bicuspid aortic valve, among others. Aortopathy is diagnosed commonly in children, from infancy through adolescence, primarily affecting the thoracic aorta, with variable involvement of the peripheral vasculature.