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Pulmonary arterial hypertension in congenital heart disease

Heart BMJ

LEARNING OBJECTIVES Review the diagnostic pathway for pulmonary arterial hypertension (PAH) in congenital heart disease (CHD). Understand and interpret right heart catheterisation data in pulmonary hypertension related to CHD. Recognise the typical presentation of PAH in patients with CHD.

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PO-01-044 ARRHYTHMIA OCCURENCE AFTER TRANSCATHETER PULMONARY VALVE REPLACEMENT IN CONGENITAL HEART DISEASE PATIENTS

HeartRhythm

Transcatheter pulmonary valve replacement (TPVR) has become a safe and effective alternative to surgical PVR in tetralogy of Fallot (TOF), isolated pulmonary stenosis (PS), and other congenital heart disease (CHD) variants.

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Raising the bar: triple therapy for pulmonary arterial hypertension associated with congenital heart disease

Heart BMJ

Pulmonary arterial hypertension related to congenital heart disease as a paradigm of complexity Pulmonary arterial hypertension related to congenital heart disease (PAH-CHD) really represents a paradigm of complexity.

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Clinical risk associated with COVID-19 among 86000 patients with congenital heart disease

Open Heart

Objective To determine the magnitude of any excess risk of mortality and hospitalisation due to COVID-19 infection in patients with congenital heart disease (CHD) in the UK healthcare system. Of patients with a positive COVID-19 test, patients with CHD were more likely than controls to be hospitalised (22.4%

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What are the Cyanotic Congenital Heart Diseases With Decreased Pulmonary Blood Flow?

All About Cardiovascular System and Disorders

Tetralogy of Fallot TOF with pulmonary atresia Pulmonary atresia with intact interventricular septum Tricuspid atresia Double outlet right ventricle Transposition of great arteries with ventricular septal defect and pulmonary stenosis Ebstein’s anomaly of tricuspid valve In DORV and tricuspid atresia, there are also variants with increased pulmonary (..)

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Triple vasodilator therapy in pulmonary arterial hypertension associated with congenital heart disease

Heart BMJ

Objective This study assessed the long-term effects of triple therapy with prostanoids on patients with pulmonary arterial hypertension associated with congenital heart disease (PAH-CHD), as there is limited information on the safety and efficacy of this treatment approach.

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Transpulmonary Expression of Exosomal microRNAs in Idiopathic and Congenital Heart Disease–Related Pulmonary Arterial Hypertension

Journal of the American Heart Association

Transpulmonary exosomal miRs offer valuable insights into pulmonary circulation microenvironments. Using an in vitro flow model simulating the shear stress experienced by pulmonary endothelial cells, we observed a significant upregulation of miR‐21.