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Arrhythmias in children undergoing orthotopic heart transplantation

Frontiers in Cardiovascular Medicine

Introduction Heart transplantation (HT) is the only treatment option in children with heart failure secondary to cardiomyopathies and non-reparable congenital heart diseases. Results We identified 27 children (66.7% On a median follow-up of 35.07 months (IQR: 13.13–111.87),

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In vivo mitral valve repair for the transplanted donor heart in orthotopic heart transplantation

Journal of Cardiothoracic Surgery

A 53-year-old woman with the dilated phase of hypertrophic cardiomyopathy underwent orthotopic heart transplantation. The donor heart was evaluated as normal preoperatively without mitral regurgitation or the.

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Genetic Contribution to End-Stage Cardiomyopathy Requiring Heart Transplantation

Circulation: Genomic and Precision Medicine

When treatable causes are excluded, studies to define causes are often abandoned, resulting in a diagnosis of end-stage idiopathic cardiomyopathy. The prevalence of causal genetic variants was significantly higher in end-stage than in previously reported ambulatory adult dilated cardiomyopathy cases (P<0.001).

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Case report of belt electrode-skeletal muscle electrical stimulation for acute heart failure with severe obesity: a novel therapeutic option for acute phase rehabilitation

Frontiers in Cardiovascular Medicine

Case presentation A 43-year-old man with a body mass index of 41 kg/m 2 was admitted to our hospital for acute heart failure due to dilated cardiomyopathy. The patient required prolonged catecholamine support owing to poor cardiac function, and heart transplantation was considered.

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Phenotypes in Arrhythmogenic Cardiomyopathy

All About Cardiovascular System and Disorders

Arrhythmogenic Cardiomyopathy was better known as Arrhythmogenic Right Ventricular Dysplasia or ARVD and sometimes as Arrhythmogenic Right Ventricular Cardiomyopathy or ARVC earlier. A study published in JACC has compared the phenotypic expression and clinical outcomes in patients with arrhythmogenic cardiomyopathy [2].

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Thirty Five Year Follow up of Three Generations of a Family with LMNA Cardiomyopathy

HeartRhythm

The clinical syndrome of combined cardiomyopathy and skeletal myopathy described in 2001 (1) was one of the initial descriptions of LMNA cardiomyopathy, a genetic variant. In 2001, genetic testing failed to detect the abnormality in this family.

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Black Families at Increased Risk of Inherited Heart Condition That Can Cause Heart Failure at a Young Age

DAIC

Researchers Elizabeth Jordan and Ray Hershberger, MD discuss the results of genetic tests that indicate a risk for dilated cardiomyopathy. The inherited heart condition often goes undiagnosed until it advances to heart failure, which is why it’s important to identify those at risk and begin treatment early.