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In vivo mitral valve repair for the transplanted donor heart in orthotopic heart transplantation

Journal of Cardiothoracic Surgery

A 53-year-old woman with the dilated phase of hypertrophic cardiomyopathy underwent orthotopic heart transplantation. The donor heart was evaluated as normal preoperatively without mitral regurgitation or the.

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Arrhythmias in children undergoing orthotopic heart transplantation

Frontiers in Cardiovascular Medicine

Introduction Heart transplantation (HT) is the only treatment option in children with heart failure secondary to cardiomyopathies and non-reparable congenital heart diseases. Results We identified 27 children (66.7% On a median follow-up of 35.07 months (IQR: 13.13–111.87),

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Genetic Contribution to End-Stage Cardiomyopathy Requiring Heart Transplantation

Circulation: Genomic and Precision Medicine

When treatable causes are excluded, studies to define causes are often abandoned, resulting in a diagnosis of end-stage idiopathic cardiomyopathy. The prevalence of causal genetic variants was significantly higher in end-stage than in previously reported ambulatory adult dilated cardiomyopathy cases (P<0.001).

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Case report of belt electrode-skeletal muscle electrical stimulation for acute heart failure with severe obesity: a novel therapeutic option for acute phase rehabilitation

Frontiers in Cardiovascular Medicine

Case presentation A 43-year-old man with a body mass index of 41 kg/m 2 was admitted to our hospital for acute heart failure due to dilated cardiomyopathy. The patient required prolonged catecholamine support owing to poor cardiac function, and heart transplantation was considered.

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Thirty Five Year Follow up of Three Generations of a Family with LMNA Cardiomyopathy

HeartRhythm

The clinical syndrome of combined cardiomyopathy and skeletal myopathy described in 2001 (1) was one of the initial descriptions of LMNA cardiomyopathy, a genetic variant. In 2001, genetic testing failed to detect the abnormality in this family.

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Abstract TP261: Stroke in pediatric heart transplant patients

Stroke Journal

Introduction:Pediatric heart transplant (PHT) recipient survival has improved. Yet, neurologic morbidity related to heart failure and its treatment persist. CHD was the pre-PHT diagnosis in 21(62%) of stroke Pts, cardiomyopathy in 12(35%) and acquired heart disease in 1(3%).

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Abstract 4134590: Procedural Related Major Adverse Events of Cardiac Catheterization in Pediatric Patients with Cardiomyopathy: Insights from IMPACT Registry

Circulation

Background:Despite the role of cardiac catheterization for hemodynamic assessment and endomyocardial biopsy (EMB) in children with cardiomyopathy, data on procedure-related major adverse events (MAE) in this population is lacking. We aim to describe the rate of MAE in children with cardiomyopathy undergoing cardiac catheterization.