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MitraClip combined with PTSBME for the treatment of obstructive hypertrophic cardiomyopathy with severe mitral regurgitation: a case report

Journal of Cardiothoracic Surgery

Hypertrophic cardiomyopathy (HCM) is the hereditary cardiomyopathy with the highest incidence rate. Its main pathological changes are ventricular septal myocardial hypertrophy and myocardial disorder, which ar.

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In vivo mitral valve repair for the transplanted donor heart in orthotopic heart transplantation

Journal of Cardiothoracic Surgery

A 53-year-old woman with the dilated phase of hypertrophic cardiomyopathy underwent orthotopic heart transplantation. The donor heart was evaluated as normal preoperatively without mitral regurgitation or the.

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Evidence of cardiomyopathy associated with Marfan syndrome in children

Heart BMJ

Objective Marfan syndrome (MFS)-associated cardiomyopathy, defined as ventricular dilation and dysfunction unexplained by volume loading, is not well defined in children. Combined mitral and aortic regurgitation indexed to LV stroke volume <20% defined absent/mild volume load. MVP may be associated with cardiomyopathy.

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Resection of hypertrophic papillary muscles and mitral valve replacement in a patient with midventricular hypertrophic obstructive cardiomyopathy – a new approach

Journal of Cardiothoracic Surgery

Midventricular hypertrophic obstructive cardiomyopathy (HOCM) is characterized by hypertrophy of the interventricular septum (IVS) and - in rare cases - of the papillary muscles (PM), which subsequently can ca.

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UH Harrington Heart and Vascular Institute First in World to Implant Penditure Clip Using Minimally Invasive Approach

DAIC

milla1cf Mon, 01/08/2024 - 14:35 January 8, 2024 — University Hospitals (UH) Harrington Heart & Vascular Institute recently became the first center in the world to implant Medtronic’s Penditure Left Atrial Appendage (LAA) Exclusion System through a minimally invasive approach during a mitral valve repair procedure.

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Medical, Surgical, and Interventional Management of Hypertrophic Cardiomyopathy

Circulation: Cardiovascular Interventions

Hypertrophic cardiomyopathy is a common but underrecognized cardiac disorder characterized by a heterogenous phenotype that includes increased left ventricular thickness, outflow obstruction, diastolic dysfunction, and arrhythmia. Hypertrophic cardiomyopathy is often heritable and associated with pathogenic variants in sarcomeric genes.

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Fabry Cardiomyopathy: Myocardial Fibrosis, Inflammation, and Down‐Regulation of Mannose‐6‐Phosphate Receptors Cause Low Accessibility to Enzyme Replacement Therapy

Journal of the American Heart Association

BackgroundThe clinical impact of enzyme replacement therapy on advanced Fabry disease cardiomyopathy appears to be limited. Controls were surgical biopsies from patients with mitral stenosis. Journal of the American Heart Association, Ahead of Print. to 19.32.1 mm in 8.61.4 of controls.